European Journal of Rheumatology
Case Report

Dermato-neuro syndrome in a case of scleromyxedema

1.

Department of Internal Medicine, Dokuz Eylül University Faculty of Medicine, İzmir, Turkey

2.

Department of Dermatology, Dokuz Eylül University Faculty of Medicine, İzmir, Turkey

Eur J Rheumatol 2015; 2: 160-162
DOI: 10.5152/eurjrheum.2015.0116
Read: 2389 Downloads: 1984 Published: 03 September 2019

Abstract

Scleromyxedema is an uncommon connective tissue disease characterized by mucin deposits, fibrosis, and proliferation of fibroblasts in the dermis. Although it shares similar sclerodermoid features, it is a different clinical entity than scleroderma. A monoclonal gammopathy is almost always present; however, progression to multiple myeloma is rare. It may have many systemic manifestations, of which the most notable being the dermato-neuro syndrome because of its rarity and potential fatal outcome. We present a case of a 50-year-old woman with scleromyxedema in whom the dermato-neuro syndrome developed.

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EISSN 2148-4279