European Journal of Rheumatology
Case Report

Therapy resistant idiopathic scleredema: an underlying pathology not always present


Department of Internal Medicine, Division of Rheumatology, Ege University Faculty of Medicine, İzmir, Turkey


Department of Rheumatology, Koç University Faculty of Medicine, İstanbul, Turkey

Eur J Rheumatol 2015; 2: 163-164
DOI: 10.5152/eurjrheum.2015.0004
Read: 2154 Downloads: 2085 Published: 03 September 2019


Scleredema is a rare connective tissue disorder of unknown pathogenesis. Three types of scleredema have been described, based on its association with postinfection, monoclonal gammopathy and diabetes mellitus. We report herein a case of scleredema which the diagnosis didn’t get specified. The patient was followed regularly for 13 years and did not respond to various combinations of immunosuppressants and psoralen plus ultraviolet A therapy. Treatment of scleredema is quite difficult and of limited success. At present, there is no proved treatment for this disease.

EISSN 2148-4279