European Journal of Rheumatology
Case Report

Catastrophic antiphospholipid syndrome: A case with unusual findings revealed in autopsy and a brief literature update

1.

Department of Internal Medicine, Hospital Universitário Clementino Fraga Filho, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brazil; Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro

2.

Department of Rheumatology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro, Rio de Janeiro, Brazil

Eur J Rheumatol 2017; 4: 281-283
DOI: 10.5152/eurjrheum.2017.17023
Read: 865 Downloads: 373 Published: 03 September 2019

Abstract

Catastrophic antiphospholipid syndrome (CAPS) is a rare and life-threatening disease. It is characterized by multiple arterial and/or venous thrombotic events, including the microcirculation, occurring in a short period, and can affect any system. Catastrophic antiphospholipid syndrome can occur in individuals with known APS under treatment, or it can be its first manifestation; in most cases, there is a triggering factor that can be identified. In this case report, we report a case of CAPS with multiple thromboses at unusual sites, including the lungs, coronary arteries, stomach, thyroid, gastrocnemius muscles, lymph nodes, and bladder, in a patient with previous diagnosis of systemic lupus erythematosus.

 

 

Cite this article as: Signorelli F, Balbi GGM, Levy RA. Catastrophic antiphospholipid syndrome: A case with unusual findings revealed in autopsy and a brief literature update. Eur J Rheumatol 2017; 4: 281-3.

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ISSN 2147-9720 EISSN 2148-4279